A19415
Size
  • 50ul
  • 100ul
Price
  • $129
  • $229
Qty
Product description

phenylalanine hydroxylase(PAH) Homo sapiens PAH encodes the enzyme phenylalanine hydroxylase that is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria. [p

Source
Rabbit
Applications
WB,IHC,ELISA
Reactivity
Human,Mouse,Rat
Dilution
WB: 1/500 - 1/2000. IHC: 1/100 - 1/300. ELISA: 1/40000. Not yet tested in other applications.
Storage
-20°C/1 year
Specificity
PAH Polyclonal Antibody detects endogenous levels of PAH protein.
Source/Purification
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
Immunogen
The antiserum was produced against synthesized peptide derived from human PAH. AA range:351-400
Uniprot No
P00439
Alternative names
PAH; Phenylalanine-4-hydroxylase; PAH; Phe-4-monooxygenase
Form
Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
Clonality
Polyclonal
Background
phenylalanine hydroxylase(PAH) Homo sapiens PAH encodes the enzyme phenylalanine hydroxylase that is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria. [p
Other
Gene_name: PAH ; Protein_name: Phenylalanine-4-hydroxylase; Expression: Liver,
Mol.Wt (Da)
10 kD
Concentration
1 mg/ml