A19189
Size
  • 50ul
  • 100ul
Price
  • $129
  • $229
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Product description

This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne

Source
Rabbit
Applications
WB
Reactivity
Human, Mouse,Rat
Dilution
WB 1:500-2000
Storage
-20°C/1 year
Specificity
This antibody detects endogenous levels of OTC at Human/Mouse/Rat
Source/Purification
The antibody was affinity-purified from rabbit serum by affinity-chromatography using specific immunogen.
Immunogen
Synthesized peptide derived from human OTC
Uniprot No
P00480
Alternative names
Ornithine carbamoyltransferase, mitochondrial (EC 2.1.3.3) (Ornithine transcarbamylase) (OTCase)
Form
Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.60% sodium azide.
Clonality
Polyclonal
Background
This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne
Other
Gene_name: OTC ; Protein_name: OTC; Expression: Brain,Liver,
Mol.Wt (Da)
127 kD
Concentration
1 mg/ml

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