

Product description
disease:Defects in MT-ATP6 are a cause of infantile bilateral striatal necrosis [MIM:500003]. Bilateral striatal necrosis is a neurological disorder resembling Leigh syndrome.,disease:Defects in MT-ATP6 are a cause of Leber hereditary optic neuropathy (LH
Source
Rabbit
Applications
IHC, ELISA
Reactivity
Human
Dilution
IHC 1:50-200, ELISA(peptide)1:5000-20000
Storage
-20°C/1 year
Specificity
This antibody detects endogenous levels of human MT-ATP8
Source/Purification
The antibody was affinity-purified from mouse ascites by affinity-chromatography using specific immunogen.
Immunogen
Synthesized peptide derived from human MT-ATP8
Uniprot No
P03928
Alternative names
ATP synthase protein 8 (A6L) (F-ATPase subunit 8)
Form
Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
Clonality
Polyclonal
Background
disease:Defects in MT-ATP6 are a cause of infantile bilateral striatal necrosis [MIM:500003]. Bilateral striatal necrosis is a neurological disorder resembling Leigh syndrome.,disease:Defects in MT-ATP6 are a cause of Leber hereditary optic neuropathy (LH
Other
Gene_name: MT-ATP8 ATP8 ATPASE8 MTATP8 ; Protein_name: MT-ATP8; Expression: Blood,Bone fossil,Bones,Breast cancer,Distant normal tissue,Endometrial adenocarcin
Mol.Wt (Da)
kD
Concentration
1 mg/ml
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